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<front>
<journal-meta>
<journal-id journal-id-type="issn">1043-3155</journal-id>
<journal-id journal-id-type="nlm-ta">Pediatr Neurol Briefs</journal-id>
<journal-id journal-id-type="pmc">pedneurbriefs</journal-id>
<journal-id journal-id-type="iso-abbrev">Pediatr Neurol Briefs</journal-id>
<journal-title-group>
<journal-title>Pediatric Neurology Briefs</journal-title>
<abbrev-journal-title>Pediatr Neurol Briefs</abbrev-journal-title>
</journal-title-group>
<issn pub-type="epub">2166-6482</issn>
<issn pub-type="ppub">1043-3155</issn>
<issn-l>2166-3155</issn-l>
<publisher>
<publisher-name>Pediatric Neurology Briefs Publishers</publisher-name>
<publisher-loc>Chicago, IL, USA</publisher-loc>
</publisher>
</journal-meta>
<article-meta>
<article-id pub-id-type="publisher-id">PNB-2013-27-7-4</article-id>
<article-id pub-id-type="doi">10.15844/pedneurbriefs-27-7-4</article-id>
<article-categories>
<subj-group subj-group-type="heading">
<subject>Myopathies</subject>
</subj-group>
<subj-group subj-group-type="Discipline-v2">
<subject>Neurology</subject>
<subject>Pediatrics</subject>
<subject>Nervous System Diseases</subject>
<subject>Child Development</subject>
<subject>Brain Diseases</subject>
<subject>Neurosurgery</subject>
<subject>Child</subject>
<subject>Infant</subject>
</subj-group>
</article-categories>
<title-group>
<article-title>Glucocorticoids for Duchenne Muscular Dystrophy</article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author" corresp="yes">
<contrib-id contrib-id-type="orcid">http://orcid.org/0000-0002-0173-7931</contrib-id>
<name>
<surname>Millichap</surname>
<given-names>J. Gordon</given-names>
</name>
<degrees>MD</degrees>
<xref ref-type="aff" rid="AF0001">1</xref>
<xref ref-type="aff" rid="AF0002">2</xref>
<xref ref-type="corresp" rid="cor1">&#x002A;</xref>
</contrib>
</contrib-group>
<aff id="AF0001">
<label>1</label>Division of Neurology, Ann &#x0026; Robert H. Lurie Children&#x0027;s Hospital of Chicago, Chicago, IL</aff>
<aff id="AF0002">
<label>2</label>Departments of Pediatrics and Neurology, Northwestern University Feinberg School of Medicine, Chicago, IL</aff>
<author-notes>
<corresp id="cor1">
<label>&#x002A;</label>Correspondence: Dr. J. Gordon Millichap, E-mail: <email xlink:href="jgmillichap@northwestern.edu">jgmillichap@northwestern.edu</email>
</corresp>
</author-notes>
<pub-date date-type="pub" publication-format="print">
<month>07</month>
<year>2013</year>
</pub-date>
<pub-date date-type="pub" publication-format="electronic">
<day>15</day>
<month>10</month>
<year>2015</year>
</pub-date>
<volume>27</volume>
<issue>7</issue>
<fpage>51</fpage>
<lpage>51</lpage>
<permissions>
<copyright-statement>Copyright: &#x00A9; 2013 The Author(s)</copyright-statement>
<copyright-year>2013</copyright-year>
<license license-type="open-access" xlink:href="http://creativecommons.org/licenses/by/4.0/">
<license-p>This work is licensed under the <uri xlink:href="http://creativecommons.org/licenses/by/4.0/">Creative Commons Attribution 4.0 International License</uri>, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.</license-p>
</license>
</permissions>
<related-article id="R1" related-article-type="commentary-article" ext-link-type="doi" xlink:href="10.1136/jnnp-2012-303902" vol="84" page="698">
<article-title>Long-term benefits and adverse effects of intermittent versus daily glucocorticoids in boys with Duchenne muscular dystrophy</article-title>
</related-article>
<abstract abstract-type="web-summary" specific-use="electronic-only">
<p>Investigators at the Dubowitz Neuromuscular Centre, Great Ormond Street Hospital, and other centers in the UK, conducted a prospective longitudinal study across 17 neuromuscular centers in the UK of 360 boys aged 3-15 years with Duchenne muscular dystrophy who were treated with daily or intermittent (10 days on/10 days off) prednisolone for a mean duration of 4 years.</p>
</abstract>
<kwd-group>
<kwd>Duchenne Muscular Dystrophy</kwd>
<kwd>Cushingoid Features</kwd>
<kwd>Glucocorticoids</kwd>
</kwd-group>
</article-meta>
</front>
<body>
<p>Investigators at the Dubowitz Neuromuscular Centre, Great Ormond Street Hospital, and other centers in the UK, conducted a prospective longitudinal study across 17 neuromuscular centers in the UK of 360 boys aged 3-15 years with Duchenne muscular dystrophy who were treated with daily or intermittent (10 days on/10 days off) prednisolone for a mean duration of 4 years. The median loss of ambulation was 12 years in intermittent and 14.5 years in daily treatment; height restriction for intermittent versus daily regimen was 1.57 (p=0.13) and the median age for loss of ambulation did not differ. Boys on an intermittent regimen declined faster than those receiving daily treatment (p&#x003C;0.001). Moderate to severe side effects were more common in the daily regimen, including Cushingoid features, hyperactive behavior and hypertension. Body mass index mean score was higher and height restriction was more severe in the daily regimen than in the intermittent regimen. [<xref ref-type="bibr" rid="CIT0001">1</xref>]</p>
<p>COMMENT. Glucocorticoids are recommended in the international standards of care guideline for DMD and benefits are confirmed by Cochrane systematic reviews [<xref ref-type="bibr" rid="CIT0002">2</xref>]. The most effective treatment postulated is prednisolone/prednisone or the equivalent deflazacort [<xref ref-type="bibr" rid="CIT0003">3</xref>]. The intermittent and daily regimens are equally effective in gain of function until 6 years of age. After age 7 years, boys on an intermittent regimen decline more rapidly than those on daily therapy. Side effects are a greater problem with daily compared to intermittent therapy.</p>
</body>
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